IPAH is a serious syndrome, with significant morbidity and mortality. It can be associated with progressive elevation of pulmonary artery pressure and can lead to right ventricular failure. By definition, the cause is unexplained and implies that associated causes of pulmonary hypertension have been ruled out. The definition, therefore, is the same as IPAH in adults: a mean pulmonary artery pressure greater than 25 mm Hg at rest with normal pulmonary capillary wedge pressure and the absence of associated causes of pulmonary hypertension. Some authors believe that including exercise hemodynamic abnormalities in the definition of IPAH is important, especially in the pediatric population; therefore, a mean pulmonary artery pressure of greater than 30 mm Hg with exercise is also considered to be an abnormal response and is consistent with the definition of IPAH.
It was suspected that I had the problem and 2 different tests indicated I did. A right heart catherization showed that I did not have it and that my lung problems were being caused by weakness of my diaphragm muscles.
If you have not seen a cardiologist then find a good one and get an appointment. I don't know enough to comment on the specifics of your results but you need to see a specialist. Your edema problems could be heart related but they are also common with lupus and kidney problems. I had a condition called proteinuria and it caused severe edema but once treated I have not had any problems at all.
Don't try to interpret your results...see a cardiologist and even a nephrologist to determine what is causing your problems.
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